In multisystem proteinopathy 1 (MSP1) caused by VCP variants, DXA scans revealed reduced bone and lean mass, and increased fat mass. This could aid in monitoring disease progression in MSP1. onlinelibrary.wiley.com/doi/10.1002/mu…

Read this AAANEM Monograph exploring the four broad indications for serial electrodiagnosis in adult peripheral neurological disorders. onlinelibrary.wiley.com/doi/epdf/10.10…

Read this Editor Choice article on adaptive cardiopulmonary exercise testing on adaptive equipment in children and adults with Friedreich Ataxia. open access for 2 months. onlinelibrary.wiley.com/doi/epdf/10.10…

Serial grip strength measurement is a feasible and objective way to assess motor strength improvement in children with CIDP receiving immunotherapy. onlinelibrary.wiley.com/doi/10.1002/mu…

NM US demonstrated nerve changes at the site of the GSW and also in the distal nerve segments including nerve enlargement, fascicular enlargement, and changes in nerve echogenicity. You can access this Editor's choice article for free for 2 months. onlinelibrary.wiley.com/doi/epdf/10.10…

Read the Editor choice from the AANEM Expert Clinical Perspective, How should newer therapeutic agents be incorporated into the treatment of patients with myasthenia gravis? available as open access for 2 months. onlinelibrary.wiley.com/doi/10.1002/mu…

Serum light chain neurofilaments can be helpful in differentiating MMN from LMN dominant ALS in those patients in whom EDX and clinical examinations remain inconclusive early in the diagnostic process. onlinelibrary.wiley.com/doi/10.1002/mu…

Read this editor choice article reporting the work of a panel of US-based expert clinicians convened to address identification, monitoring, and treatment of HTTR amyloid neuropathy. Available for free for 2 months at pubmed.ncbi.nlm.nih.gov/38174864/

Read this Editor Choice article, free for 2 months, validating MAGNET for rapid use during clinical evaluations for distal sensory/autonomic (small fiber) neuropathy. onlinelibrary.wiley.com/doi/epdf/10.10…

Editor's choice article for free for 60d on the comparison of needle EMG and muscle US utility. They typically produce disparate results and identify different pathologies reporting that muscle US is less suited for detecting mild neurogenic abnormalities. onlinelibrary.wiley.com/doi/epdf/10.10…

Artificial intelligence (AI) distinguished between EMG signals in normal individuals and ALS and myopathy, with 67-99.5% accuracy. This M&N review explores the immense potential that AI holds in EDX and neuromuscular US. onlinelibrary.wiley.com/doi/epdf/10.10…

Read the 2nd Editor Choice article: long-term safety and functional outcomes of delandistrogene moxeparvovec gene therapy in patients with DMD: A phase 1/2a nonrandomized trial, Full text is available for 2 months at onlinelibrary.wiley.com/doi/10.1002/mu…

Read the Muscle and Neeve Editor's Choice article, available as full text for 2 months. Single institution experience with efgartigimod in patients with MG: Patient selection, dosing schedules, treatment response, and adverse events. onlinelibrary.wiley.com/doi/10.1002/mu…

Based on data from insurance claims, the prevalence and incidence of diagnosed MG in the US in 2021 were calculated to be 37.0 per 100,000 persons and 3.1 per 100,000 persons, respectively. onlinelibrary.wiley.com/doi/epdf/10.10…

In this retrospective study, considering the “possible CIDP” category, the EAN/PNS 2021 criteria had lower sensitivity than the EFNS/PNS 2010 criteria (78% vs. 93%), whereas its specificity was higher (78% vs. 61%). onlinelibrary.wiley.com/doi/full/10.10…

Diaphragmatic EMG is challenging, require experience, and risky. US was introduced as an adjuvant technique available at the bedside that increases the sensitivity and specificity of the EDX evaluation of respiratory symptoms. Read the AANEM monogram at onlinelibrary.wiley.com/doi/10.1002/mu…

In this retrospective study of 159 patients with isolated femoral neuropathy, the most common etiologies were compressive (40%) and perioperative stretch (35%). Although motor recovery is common, improvement is often prolonged and incomplete. onlinelibrary.wiley.com/doi/10.1002/mu…

In this retrospective study on 502 patients, mostly referred for mononeuropathy, plexopathy, and polyneuropathy, high resolution US was abnormal in 81.7%. It added additional useful information in 79.0% and was decisive in management in 62.7%. onlinelibrary.wiley.com/doi/epdf/10.10…

Hourglass-like constrictions on MRI are common in electromyography-confirmed cases of neuralgic amyotrophy (Parsonage–Turner syndrome)

Anti-MAG neuropathy features a progressive ataxia and distal sensory loss. EDX shows distally accentuated CV slowing. The slow nature of the disease presents unique challenges when trying to find effective therapeutics. Read this M&N review on the topic onlinelibrary.wiley.com/doi/epdf/10.10…